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A CASE REPORT OF LIMB-BODY WALL COMPLEX MALFORMATION.

JOTHI GANESH R

Abstract


During routine antenatal checkup, a 24 year old  primi-gravida was observed to have a 20 weeks old fetus with abdominoschisis with liver and intestinal contents herniating through the midline defect, amelia (absence of right upper limb) absence of sternum, thoracic scoliosis and congenital talipes equinovarus of right foot were noted. There was no history of consanguinity or family history of any malformations. There was no history of intake of drugs other than iron and calcium  supplements during the pregnancy. After medical termination of pregnancy, on gross examination of the expelled fetus the above mentioned conditions were confirmed and a diagnosis of Limb Body Wall Complex Malformation was given.

 


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References


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