A CASE OF JUVENILE DERMATOMYOSITIS WITH PERITONEAL CALCIFICATION

Abstract

Juvenile Dermatomyositis is a multisystem
disease characterized by acute and
chronic nonsuppurative inflammation of
skin and striated muscle. Calcinosis is
one of the hallmark squeal of juvenile
dermatomyositis, and despite recent progress
in the therapy of these disorders,
dystrophic calcification still occurs in approximately
one-third of patients. Ectopic
calcification in JDM is thought to develop
through a dystrophic mechanism. The
sites most frequently affected are the elbows,
knees, digits and extremities, although
it may occur virtually anywhere
over the body. This complication can
cause significant debility with severe
pain, skin ulceration, muscle atrophy,
joint contracture, and acro osteolysis. Although
various clinical patterns of calcification
have been described peritoneal
calcification is not reported so far. We
report a case of Juvenile Dermatomyositis
with extensive visceral peritoneal calcification.