BRONCHOPULMONARY FOREGUT MALFORMATION TYPE III CASE SERIES OF AN OFTEN MISDIAGNOSED ENTITY

Abstract

Pulmonary sequestration occurs when a                disturbance in embryonic development produces a cystic mass of nonfunctioning lung tissue. Most often the mass is supplied by an anomalous systemicartery and has its own bronchial system, which usually does not communicate with the normal bronchial tree. Though traditionally classified as intralobar (ILS) and extralobar (ELS) sequestrations, it is  postulated that they belong to a broad spectrum of           bronchopulmonary-foregut malformations. These              Bronchopulmonary foregut malformations were classified by Shrikant et al and our discussion is pertaining to type III of this set of malformations. The treatment of ILS in adults is often misdiagnosed and hence delayed. We present a case series of six cases over the last five years. All of these cases were on medical management before they presented to our          hospital and on presentation to us they were diagnosed to have communicating bronchopulmonary foregut malformation type III. Of these 5 cases were surgically treated while one patient was lost in follow up as he was not willing for surgery.