RUPTURED LIVER ADENOMATOSIS - Report of a rare case
Abstract
Solitary hepatic adenoma is a rare tumor
and adenomatosis of liver is even rarer.
Liver adenomatosis was first recognized
by Flejou et al as more than 10 adenomas
in otherwise normal liver. Although a
benign disease, liver adenomatosis can
be associated with potentially fatal complications
such as spontaneous bleeding
due to rupture and malignant transformation.
The natural history, etiology, optimal
management and prognosis are not yet
well defined due to rarity of the disease.
However, most authors recommend surgical
removal of large or complicated tumor
in symptomatic patient whereas,
close follow-up in asymptomatic patients
with small tumor. We report a 31-year old
lady who was found to have 8 adenomas
in otherwise normal liver. She presented
with sudden onset abdominal pain secondary
to spontaneous bleeding due to
rupture. Hematoma evacuation and right
hepatectomy was done and her follow-up
has been uneventful and symptom-free.
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