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SPINAL INTRADURAL EXTRAOSSEOUS EWINGS SARCOMA - A CASE REPORT

KATHIRVEL CHELLAIAH

Abstract


Extraosseous Ewings sarcoma (EES)
involving the central nervous system is
rare. We present an unusual case of a
primary extraosseous Ewings sarcoma
arising from the spinal intradural extramedullary
space, based on imaging,
histopathological, and immunohistochemistry.
A 15-year-old girl was admitted
in the hospital with both lower limb
pain for 3 months and weakness of both
lower limbs for 2 months. Our provisional
diagnosis based on clinical and radiological
investigation was an intradural extramedullary
space occupying lesion extending
from D11 to S1 probably a malignant
peripheral nerve sheath tumor or
lymphoma. Since we thought of malignant
lesion we proceeded with biopsy of
the lesion through laminectomy at D12
level. Histopathologically reported as Ewings
tumor and that was confirmed with
immunohistochemistry study CD 99.The
patient was treated with
Chemo and radiotherapy.It has been reported
that extraosseous cases of Ewings
tumor is rare and reported in extradural or
paravertebral area but intradural Ewings
tumor is quite rare.


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