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ORAFACIAL DIGITAL SYNDROME— TYPE I: A RARE CASE REPORT WITH MULTIDISCIPLINARY TREATMENT.

SENTHIL KUMAR SARAVANAN,KAYAL louis ,MUR .

Abstract


Orofacial Digital syndrome –Type I  is an X-linked dominant disease affecting both male and female . It presents with distinct malformations in the oral cavity and defects in the face and digits of the upper and lower extremities. Early and Accurate diagnosis and multidisciplinary approach is required by allied health professionals is to plan out a systematic           management protocol in these victims in order to minimize future odontogenic problems ,related skeletal and systemic problems. The objective of this article is to report a rare case of Orofacial Digital syndrome in a 6 year old female  child  ,with characteristics features of Orofacial syndrome             –type I and treatment undertaken to minimize the orofacial problems.

 


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References


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