A CASE REPORT OF PEUTZ -JEGHERS SYNDROME PRESENTING AS MULTIPLE INTUSSUSCEPION
Abstract
Abstract : Peutz-Jeghers syndrome is a rare familial autosomal dominant disorder. Peutz -Jeghers syndrome in a young girl presented as multiple intussusceptions involving small bowel. Complaints were intermittent abdominal pain with minimal abdominal signs. She was managed with laparotomy, and the findings were three intussusceptions involving the ileum. Peutz- Jeghers syndrome itself rare which presented as three intussusceptions with subtle signs of obstruction is rare.
Keyword : Peutz - Jeghers syndrome, Intussusception, hamartamatous polyp, entrostomy, laparotomy
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