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A CASE REPORT OF PEUTZ -JEGHERS SYNDROME PRESENTING AS MULTIPLE INTUSSUSCEPION

NIVAS .

Abstract


Abstract : Peutz-Jeghers syndrome is a rare familial                  autosomal dominant disorder. Peutz -Jeghers syndrome in a young girl presented as multiple intussusceptions involving small bowel. Complaints were intermittent abdominal pain with minimal abdominal signs. She was managed with               laparotomy, and the findings were three intussusceptions involving the ileum. Peutz- Jeghers syndrome itself rare which presented as three intussusceptions with subtle signs of       obstruction is rare.

Keyword : Peutz - Jeghers syndrome, Intussusception, hamartamatous polyp, entrostomy, laparotomy

 


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