A RARE TUMOR (ROSAI DORFMANS DISEASE) OF INFRATEMPORAL FOSSAA Case Report.

Abstract

Abstract : Rosai dorfmans disease is otherwise known as
sinus histiocytosis with massive lymphadenopathy is a
rare ,idiopathic, benign disorder of reticuloendothelial system
that causes painless cervical lymphadenopathy. The
extranodal manifestation of the disease which is very rare.
Here we report a similar case of 26 year old male with right
infratemporal fossa mass extending to lateral orbit,which on
radiological investigations came to differential diagnosis of
L y m p h o m a , G r a n u l o m a t o u s
lesion, Schwannoma, Tuberculosis ,Sarcoidosis. All speciality
opinion were inconclusive and no improvement on medical
management.Then we decided for the excision of the mass
through an external approach. The post operative HPE report
came as Rosai Dorfman Disease.
Keyword : Rosai-Dorfman Disease, sinus histiocytosis,
emperipolesis, extranodal, pterygopalatine fossa