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POLYOSTOTIC MELORHEOSTOSIS OF HAND - A RARE CASE REPORT

SELVAKUMAR SRINIVASAN

Abstract


Melorheostosis is a rare sclerosing
skeletal dysplasia affecting bones of the
appendicularskeleton. Radiography
shows the characteristic dribbling candle
wax appearance and streakyendosteal
bone formation. Soft tissue calcification
and even ossification may rarely be
seen.Radiological appearance forms the
basis of the diagnosis, as clinical and
histological findings arenon-specific. This
is the first reported case of melorheostosis
in this part of the country among
theliterature known to us. We present a
case report of a 26 year old woman, who
was diagnosed withmelorheostosis affecting
the left hand. The purpose of this
case report is to describe the presentationof
the disease and the principles of
treatment, because the patients symptoms
vary considerably inmelorheostosis
and consequently their treatment should
be individualized.


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