AN INTERESTING CASE OF JEJUNO-JEJUNAL INTUSSUSCEPTION IN A KNOWN CASE OF JUVENILE POLYPOSIS SYNDROME

Abstract

Abstract : Juvenile polyposis syndrome
(JPS) is charecterised by predisposition
to hamartomatous polyps in the gastrointestinal
tract,specifically in the stomach,
small intestine,colon and rectum.The
term juvenile refers to the type of polyp
rather than the age of onset.Most individuals
with Juvenile polyposis syndrome
have some polyps by the age of 20
years,some may have only 4 or 5 polyps
over their life time where as others in the
same family may have more than hundred.
If polyps are left untreated it may
cause anemia , bleeding and complications
like intussusception.Most juvenile
polyps are beningn,however malignant
transformation can occur.Risk of gastrointestinal
cancers ranges from 9 to 50
percentage.Most of the increased risk is
attributed to colon cancers.Here I am
presenting an interesting case of Juvenile
polyposis syndrome who presented
with clinical features of acute intestinal
obstruction and on laparotomy found to
be a case of jejuno-jejunal intussusception
Keyword :Juvenile polyposis syndrome,
jejuno-jejunal intussusception