Angiosarcoma in chronic lymphedema a rare case of Stewart-Treves syndrome
Abstract
The Stewart-Treves Syndrome is defined
as an angiosarcoma (very aggressive
malignant tumor originating from endothelial
cells) appearing in a specific clinical
setting. This tumor develops in patients
suffering from chronic lymphedema.
The diagnosis relies on medical
history, clinical examination and histological
assesment (biopsy or resection).
This syndrome represents a rare clinical
entity. It mostly arises from lymphedema
induced by radical mastectomy in breast
cancer patients. Unfortunately, the prognosis
is poor. A large surgical resection
is the treatment of choice, if the patient is
a candidate for surgical resection with a
curative intent. Radiotherapy is sometimes
used as a palliative local treatment.
Chemotherapy is only used in more advanced
cases, not curable by surgery
alone. We report a case of angiosarcoma
in long standing filarial lymphedematous
lower limb in a female patient.
Keyword : Angiosarcoma, chronic lymphedema,
Stewart-Treves Syndrome, filarial leg
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