SMALL BOWEL LEIOMYOMA IN A PATIENT WITH NEUROFIBROMATOSIS - A CASE REPORT AND REVIEW OF LITERATURE
Abstract
Neurofibromatosis, an autosomal dominantly
inherited disease occurs 1 in 3000
live births. The disease has varied manifestations
in the skin, nervous tissue,
bone and soft tissues. Gastrointestinal
tract may also be involved with multiple
Neurofibromas, giving rise to obscure
gastrointestinal bleeding and obstruction.
There is an increased association between
benign small bowel Leiomyomas
and Neurofibromatosis but this has been
documented in very few instances. Due
to its rarity, a high degree of suspicion for
gastrointestinal tumor in patients with
Neurofibromatosis is needed for timely
diagnosis.Present report describes an
interesting case of a small intestinal Leiomyoma
in a patient with cutaneous Neurofibromatosis
.
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