RECURRENT EXTRA OSSEOUS EWING'S SARCOMA LEFT ARM - A CASE REPORT

Abstract

Extraosseous Ewings Sarcoma is a rare
malignant small round cell neoplasm of
undifferentiated mesenchymal origin.
Most commonly affects children and age
group less than 20. Ewings sarcoma, Extraosseous
Ewings saroma, Primitive
neuro ectodermal tumour(PNET), Aesthesioblastoma,
Askin tumour(PNET of
chest wall) are all belongs to Ewings
family of tumour (EFT). Less than hundred
cases are reported all over the
world. t(11 22)(q24 q12) translocation is
common. A 27 year male presented with
swelling in the left arm for past 6
months.1 year before excision biopsy
done for swelling in the same region.
MRI shows swelling in the subcutaneous
plane, Biopsy shows EwingsPNET. CT
chest normal. Wide local excision with
latismus dorsi flap and split skin graft
done followed by chemotherapy. Histopathology
report came as small round
cell with scanty cytoplasm and hyperchromatic
nuclei with mitosis,CD 99 positivity
suggestive of Ewings Sarcoma.
On follow up for 1 year with no evidence of
recurrence metastasis.