Clear cell sarcoma or Malignant melanoma of soft part - a rare entity

Abstract

Clear cell sarcoma is an extremely rare,
slow growing and aggressive soft tissue
sarcoma with melanocytic differentiation.
We report a case of recurrent clear cell
sarcoma treated at our Institute for its
rarity and need for appropriate diagnosis
and treatment. A 26 year old male presented
to our Institute with recurrent
swelling in the right popliteal fossa for 1
month duration. He had previous excision
of the right popliteal fossa lesion
and reported as alveolar rhabdomyosarcoma
outside and he came to our Institute
for further treatment. On evaluation
he was diagnosed with non-metastatic
recurrent clear cell sarcoma of the right
popliteal fossa. He had right popliteal
fossa exploration and underwent right
above knee amputation in view of popliteal
vessel and nerve involvement. He
had an uneventful recovery and is receiving
ifosfamide and doxorubicin based adjuvant
chemotherapy. Clear cell sarcoma
is a rare melanin producing soft tissue
sarcoma with diagnostic challenge. Complete
surgical excision is
the optimal treatment for local control.
Keyword :Sarcoma, clear cell, melanoma