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A Rare Case of Fibrous Dysplasia of Ethmoid Sinus – A Case Report & Review of Literature

Tasneem Syed Fiaz Ahmed, Indra T .

Abstract


Introduction: Fibrous dysplasia is a benign skeletal   lesion where the normal medullary bone is replaced by immature and fibrous stroma due to abnormal osteoblastic differentiation of unknown etiology.

 Case report : A 43 year old female with complains of nasal  obstruction and anosmia found to have a bony hard mass between septum and middle turbinate. CT scan showed a fibroosseous lesion of ethmoid with ground glass  appearance. Biopsy confirmed fibrous dysplasia.     Endoscopic removal of mass was done.

 Discussion:Fibrous dysplasia mostly occurs in the long bones, craniofacial bones are second common site of involvement. Fibrous dysplasia of paranasal sinus is rare. Conservative surgery is indicated for symptomatic          patients.

 Conclusion: Fibrous dysplasia is a rare disease of  ethmoid sinuses. In limited lesion, an endoscopic sinus surgery could serve as an optimal treatment of choice.

 Keywords: Fibrous dysplasia, Ethmoid


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References


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