Sjogren syndrome with Hypokalemic Quadriparesis diagnosed in pregnancy - a case report of the pregnancy outcome

Hemlatha T .

Abstract


Sjogren syndrome is one of the rarely reported autoimmune disorders in pregnancy. In this condition ,the individuals immune system mistakenly attacks its own moisture producing glands with a progressive degeneration of the exocrine glands. We report a case of a 29 yr old pregnant woman,G4P1L0A2, who presented with acute quadriparesis, distal renal tubular acidosis and severe hypokalemia in the twelfth week of her pregnancy. The patient was then evaluated and diagnosed with SJOGRENs SYNDROME with anti SS(RO) and antiSS(LA) POSITIVE and ANA POSITIVE. She was a case of bad obstetric history with 2 abortions and a neonatal loss due to fetal bradycardia attributed to congenital heart block. Patient was followed up regularly and has successfully delivered at term an alive boy baby weighing 2.450kg by LSCS. we report this case for its rarity and the good fetal outcome.

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References


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