Hernia Uteri Inguinalis

Abstract

A 50 year-old male presenting with left sided obstructed inguinal hernia was found to have uterine tissue extending through the inguinal canal, warranting a diagnosis of persistent Mullerian duct syndrome (PMDS). PMDS is an extremely rare form of internal male pseudo-hermaphroditism in which female internal sex organs, including the uterus, fallopian tube, persist in a 46XY male with normal external genitalia. The condition results from a congenital insensitivity to anti-Mullerian hormone, or lack of anti-Mullerian hormone, leading to persistence of the female internal sex organs in a male. Patient taken up for emergency surgery.On exploration of scrotum revealed small bowel along with it rudimentary uterus and fallopian tube without ovary was found. It was excised , the operation was completed by left inguinal herniorraphy and its contents confirmed by histopathology report. Opposite scrotum and testis was found to be normal.