ERLYN WERNER WUNDERLICH SYNDROME - A RARE CASE REPORT

Abstract

Herlyn Werner Wunderlich syndrome is a rare congenital mullerian anomaly characterized by uterus   didelphys with obstructed hemivagina and ipsilateral renal agenesis. It is usually present after menarche with  progressive pelvic pain during menstruation secondary to hematocolpos. Awareness is necessary in order to diagnose and treat this disorder properly before complication occurs. MRI is the preferred investigation of choice to delineate uterine malformation. When genital anomalies are  encountered, a screening should also be made for congenital anomalies of renal tract and vice versa. We describe below the evaluation and surgical management of a 13 year old girl with the above condition who was diagnosed initially using ultrasound and later confirmed by using MRI. Resection of vaginal septum was done for obstructed right sided hemivagina.