A RARE CASE OF SOLITARY DUMBELL RETROPERITONEAL NEUROFIBROMA

Abstract

Neurofibroma may arise in any part of the body and is commonly a feature of generalised neurofibromatosis with skin lesions, but it also occurs as a solitary tumour  without any findings of cafeulait spots or family history. Abdominal involvement occurs in the form of neurofibroma in the liver, mesentery, retroperitoneum, gastric and bowel. 76yr old female patient came to our OPD with complaints of  swelling in the abdomen and right thigh for the past 1year.Ho pain over swelling in thigh for past 6 months, no ho abdominal pain or distension and any disturbance in bowel and bladder habits. On examination there was a mass of size 10x8 cm in the RIF and Right Lumbar region of the abdomen which does not moves with respiration, variable in consistency and lower border not felt and a swelling of size 10x6 cm in the upper aspect of right thigh which was variable in consistency. USG abdomen showed 13x12cm cystic mass lesion anterior to right psoas and USG thigh showed 16x9cm cystic lesion in anterior compartment of right thigh. CT abdomen shows large abdominopelvic cystic lesion extending into thigh along  muscle plane. CT thigh shows large cystic lesion in anterior aspect of  right thigh in muscle plane. FNAC revealed spindle cell lesion with myxoid change. Surgical excision was done. HPE showed Neurofibroma with myxoid change.  Immunohistochemistry showed S-100 positive.