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A CASE REPORT OF BILATERAL RETINITIS PIGMENTOSA WITH CENTRAL AREOLAR CHOROIDAL DYSTROPHY

RAGHURAM V

Abstract


Retinitis Pigmentosa with Central Areolar    Choroidal Dystrophy is a rare clinical condition. We present a 65 years old male with defective vision on both eyes for the past 3 years and it was progressive in nature, on further evaluation the patient gives a history of noticing night             blindness for the past 20 years. Fundus examination on both eyes show waxy pale disk and retinal pigmentary changes in all four quadrants with reduced arterial calibre. At macula of both eyes, oval shaped geographic depigmentation with  atrophy of retinal pigment epithelium chorio capillaries was noted. No further intervention was suggested because of the poor visual outcome. To the best of our knowledge, the               present case report is the first to describe co-existence of Bilateral Retinitis Pigmentosa with Central Areolar Choroidal Dystrophy.

 


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