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A CASE REPORT OF PERIAMPULLARY ADENOCARCINOMA IN A PATIENT WITH VONRECKLINGHAUSENS DISEASE (NEURO FIBROMATOSIS TYPE 1)

DHANA SEKAR A

Abstract


Adenocarcinoma of the gastrointestinal tract are relatively rare in patients with Vonrecklinghausens disease also known as Neurofibromatosis type1 and periampullary adeno carcinoma are extremely rare in Vonrecklinghausens disease. Vonrecklinghausens disease is an autosomal dominant genetic disorder with a known predisposition to gastro intestinal neoplasm such as carcinoids and stromal tumours. I am presenting a case report of 47 year old male Mr.Rangaswamy with Vonrecklinghausens disease with            periampullary adenocarcinoma presenting with clinical   features of obstructive jaundice

 


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References


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