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Retrobulbar haemorrhage in a Factor XIII deficiency patient a case report



Factor XIII deficiency is a rare bleeding disorder with an incidence of one in 2.5 million population. It presents with prolonged umbilical cord stump bleeding during neonatal period, delayed soft tissue bruising, mucosal bleeding and with life- threatening intra cranial haemorrhage. Here report a 14 years old boy, known case of factor XIII deficiency           presented with acute proptosis and defective vision in the Right eye following Road Traffic Accident, diagnosed to have Retrobulbar haemorrhage, who was immediately underwent for hematoma evacuation with lateral canthotomy under           general anesthesia and he received 6 units of cryoprecipitate before and after the procedure as per Hematologist                instruction.Postoperatively, the retrobulbar hemorrhage         regressed and vision improved to 6 6p


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