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INCONTINENTIA PIGMENTI- A CASE REPORT

PRIYANKA S

Abstract


Incontinentia pigmenti (Bloch Sulzberger   syndrome), a rare, hereditary syndrome inherited by X-linked dominant gene, primarily affects female infants and is lethal in males. Two cases are reported here, the older child was in the third stage- pigmented stage and the newborn was in the first stage- vesicular.

 


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References


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Rook's book of dermatology

Nelson Textbook of Pediatrics


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