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MELORHEOSTOSIS - A RARE CASE REPORT

KALAIYARASAN T

Abstract


ABSTRACT Introduction Melorheostosis(synonyms candle bone disease, melting wax syndrome, Leri disease) is a rare chronic bone disorder, first described in 1922 by Leri and Joanny. Men and women are equally  affected, and no hereditary features have been discovered. Onset is insidious, and most common symptom is pain. Most common part of bone is diaphysis of the long bone of lower limb rarely the axial skeleton. Classical radiological   appearance of flowing hyperosteosis resembling hardened wax that has dripped down the side of a candle. Case Report A 30 years old man presented with right leg pain with mild swelling and limitation of knee movement. On examination non tender bony hard swelling, hyper pigmented and  restriction of knee movement present. Plain radiographs showed extensive, dense, undulating or irregular cortical hyperostosis, resembling candle wax, extending along the length of bone.. Conclusion. The exact aetiology remains unclear. There is no definite treatment available for this  disease. Only symptomatic treatment improves the condition of the patients.

 


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References


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