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A RARE CASE OF EVANS SYNDROME

VALARMATHI M

Abstract


Evans syndrome is a very rare autoimmune disorder in which the immune system destroys the bodys red blood cells, white blood cells and platelets. Affected people often experience thrombocytopenia and coombs positive haemolytic anaemia. Here we report a case of 12 years old girl presented with fever for 15 days with severe anaemia and thrombocytopenia. Later on, the child developed                     hemoglobinuria, malena, diffuse rash and                             hepatosplenomegaly. Her investigations revealed positive direct coombs test, ANA, anti ds DNA. So, the diagnosis of Evans syndrome was made.

 


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References


Josephine pasangna ,chooi Bee LIM ,Lajin Indon, et al.significance of autoimmune haemolytic anemia and immune thrombocytopenia (Evans syndrome) in SLE.Malaysian J Pathol 1994,16(1)19-82

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Ware, Russel.E, Donald H Mahony and Stephen A Landlaw “AIHA in children”. upto- date (2012)

Nortan A, Robert I. Management of Evan syndrome.Br J Hematol 2006:132:125


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