A case report - Congenital Cutaneous Kaposiform haemangioendothelioma.

Abstract

Kaposiform haemangioendothelioma is a
rare, locally aggressive vascular lesion ofinfancy
and childhood, often associated
with Kasabach- Merritt syndrome and lymphangiomatosis(
1,2).Despite the rarity of
this lesion, the morphological and clinical
appearancesdistinguish it from other mimics(
2,3) . As congenital form of haemangioendothelioma
is very rare (3), it preluded
the reporting of this case. This case
is a male infant born with a large violaceous
patch over the right loin extending
to the back measuring about 12x8cm. No
similar or deep lesions were found elsewhere.
Incisional biopsy revealed the diagnosis
of Kaposiform haemangioendothelioma.
The tumor was immunoreactive
to CD31 and CD34. A late onset of Kasabach-
Merritt syndrome was noted.