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SACRAL DYSGENESIS WITH ANO-RECTAL MALFORMATIONS

MANIMEGALAI S

Abstract


Sacral dysgenesis manifests as dysplasia, hypoplasia or absence of sacral vertebrae. Sacrum is derived from medio ventral portions of somites 30-35, which forms a series of ossification centres that are initially visualized as  radiographic opacities by 14 wks of gestation. Sacral dysgenesis usually occurs in association with other anomalies like VACTRL Association and Asymmelia. Sacral dysgenesis with ano-rectal malformations was observed in one spontaneously aborted fetus of 20 wks. Such type of anomalies is very rare and is clinically important for surgeons and  pediatricians.

 


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References


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