PARATESTICULAR EMBRYONAL RHABDOMYOSARCOMA - A RARE CASE REPORT

Abstract

Introduction Rhabdomyosarcomas comprise the   single largest category of soft tissue sarcomas in children and adolescents. Embryonal paratesticular rhabdomyosarcoma is a very rare mesenchymal tumor. It is an intrascrotal tumor that is localized in paratesticular structures such as the epididymis or spermatic cord. Case presentation - Our patient was a 16-year-old boy, who presented with a painless left scrotal mass that had evolved over two months. Thoracoabdominopelvic CT scan revealed a presumptive diagnosis of a testicular tumor with secondries. A left sided high inguinal orchidectomy was performed. The histopathological examination of the excised tissue provided the diagnosis of an Embryonal rhabdomyosarcoma. His serum markers for alpha- fetoprotein, human chorionic gonadotropin and lactate dehydrogenase were normal. The patient was followed up postoperatively with  chemotherapy. Vincristine, doxorubicin and cyclophosphamide (VAC) regimen was used and he is showing good clinical          improvement. Conclusion - Paratesticular embryonal     rhabdomyosarcoma is a rare aggressive tumor manifesting in children and very young adults. A well-defined treatment based on surgery and chemotherapy yields good results.