BILATERAL WILMS TUMOUR AND NEPHROBLASTOMATOSIS

Abstract

Wilms tumor (Nephroblastoma) is a common  pediatric tumor, with peak incidence at 3-4 years of age and accounts for 87 percentage of pediatric renal masses. The incidence is approximately 1 in 10,000 populations (1, 2, and 3). Wilms tumor is bilateral in 4-13 percentage of children (6).Metanephric blastema that persists at birth is called a nephrogenic rest, in addition malignant transformation of nephrogenic rest is likely to occur in less than 1 of these  affected children. Multiple nephrogenic rests are referred to as nephroblastomatosis. Bilateral perilobar nephrogenic rests and Wilms tumor, without any associated syndrome is a rare entity.