A RARE CASE OF NON COMPACTION OF RIGHT VENTRICLE
Abstract
Isolated ventricular non compaction is a
rare type of cardiomyopathy with uncertainetiology
.This results from arrest of
ventricular compaction of myocardium
during embryogenesis.This disorder is
diagnosed mainly by transthoracic echocardiography
by presence of excessive
prominent trabeculations with deep intertrabecular
recesses.Magnetic resonance
imaging is needed in some cases for
confirming the diagnosis.Clinical manifestations
include heart failure, atrial and
ventricular arrhythmias,embolic
events.Usually left ventricle is involved in
majority of patients, isolated rightventricle
involvement has been reported
rarely.Here we report a case of isolated
right ventricular noncompaction in a 19
year old male who presented with severe
right heart failure and atrial fibrillation.
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