DOWLING- DEGOS DISEASE- A CASE SERIES
Abstract
Abstract : Dowling Degos Disease or Reticular pigmented
anomaly of flexures, is a rare autosomal dominant pigmentary
disorder characterized by acquired reticulate pigmentation of
flexures, groin, neck. We describe a series of 6 cases of
Dowling Degos disease belonging to 5 separate families
presenting over a period of two years. These cases have
been proven by histopathology. We present this case series
as this disease might not be as rare as it has been reported
so far. This is probably because Dowling Degos Disease is
easily missed.
Keyword :Reticular pigmented anomaly of flexures,
Autosomal dominant.
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