Parry-Romberg syndrome and En Coup de Sabre overlap
Abstract
Abstract : Parry-Romberg syndrome (PRS) and En Coup de
Sabre (ECDS) type of morphoea has been reported
sporadically in literature. We report a 30 year old female
patient who presented with a purplish pigmented sclerotic
plaque on the right side of face and scalp with obvious facial
asymmetry. Additionally she had facial muscle tightness,
migraine and myopia in the right eye. A provisional diagnosis
of Parry-Romberg syndrome with En Coup de Sabre of
morphoea was made.
Keyword :''Parry-Romberg syndrome'', ''Progressive facial
hemi atrophy'', ''En Coup de Sabre''.
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PDFReferences
Tony Burn, Stephen Breathnach, Neil Cox, Christopher Griffiths,
Rooks text book of Dermatology, 8 th ed. Oxford University
press;2010.p.45.11-12.
Thomas J.A. Lehman, Scleroderma en Coup de Sabre
and Parry Romberg Syndrome Not Just Growing Pains: A
Guide to Childhood Muscle, Bone, and Joint Pain,
Rheumatic Diseases, and the Latest Treatments current
edition oxford university press; 2004.p.204-5.
Maletic J, Tsirka V, Ioannides P, Karacostas D, Taskos
N. Parry-Romberg Syndrome Associated with Localized
Scleroderma. Case Rep Neurol.2010;2:57-62.
Thilo Gambichler, Alexander Kreuter, Klaus Hoffmann,
Falk G Bechara, Peter Altmeyer and Thomas Jansen.
Bilateral linear scleroderma "en coup de sabre" associated
with facial atrophy and neurological complications. BMC
Dermatology 2001;1:9.
Tameka K Lane MD, Jessie Cheung MD, Julie V Schaffer
MD Parry-Romberg syndrome with coexistent morphea.
Demrmatology Online 2008;14:21.
Jon Stone -Parry-Romberg syndrome. Neurological
Rarity. Practical Neurology 2006;6:185-188.
Stone J. Parry-Romberg syndrome: a global survey of
patients using the Internet. Neurology. 2003;61:674–
Tollefson MM, Witman PM. En coup de sabre morphea
and Parry-Romberg syndrome: a retrospective review of 54
patients. J Am Acad Dermatol. 2007;65:257– 263.
Auvinet C, Glacet-Bernard A, Coscas G, Cornelis P,
.cadot M, Meyringnac C.Parry-Romberg progressive facial
hemiatrophy and localized scleroderma.
Henry Foong, En Coup De Sabre in a young woman,
Virtual grand rounds in dermatology. Available at: http://
www.vgrd.org/archives/cases/2008/sabre/sabre.html.
Blaszczyk M, Janninger KC, Jablonska S; Childhood
scleroderma and its pecularities; Cutis 1996; 58: 141-154.
Feroze Kaliyadan, Kabiri Biswas, AD Dharmarathnam.
Progressive facial hemiatrophy- a caseseries. Indian Journal
of Dermatology,2011;56:557-560.
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