Congenital generalized linear porokeratosis with nail dystrophy A case report
Abstract
Abstract : Linear porokeratosis is a rare disorder of
keratinization (3.5 - 16.7 of five clinical variants) which usually
appears at birth (1). We report a case of 11 year old female
patient with generalized linear porokeratosis, a very rare
variant with extensive involvement of trunk and extremities
with nail involvement.
Keyword :Linear porokeratosis, nail dystrophy, cornoid
lamella
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