DOWLING DEGOS DISEASE WITH RETICULATE ACROPIGMENTATION OF KITAMURA A CASE REPORT
Abstract
Abstract : INTRODUCTION Dowling Degos Disease (DDD)
and Reticulate Acropigmentation of Kitamura (RAPK) are rare
autosommal dominant disorders. In DDD heavily pigmented
macules are arranged in a reticular pattern with a tendency to
coalesce on flexural skin. Extensive areas of skin may be
affected. RAPK presents as slightly depressed
hyperpigmented macules on dorsa of hands and feet that
evolve into a reticulate pattern. Palmoplantar pits may be
associated with RAPK.CASE REPORT A 40 year old female
presented with hyperpigmented macules for 10 years. Family
history of similar lesions was present. Dermatological
examination revealed hyperpigmented macules on limbs,
trunk and thighs, axilla, neck, groin, more pronounced over
flexures with reticulate pattern in certain areas. Patient also
had pitting of palms and soles. Biopsy taken from
hyperpigmented macule had features consistent with
DDD.DISCUSSION DDD and RAPK diseases may appear
together supporting the concept that they aredifferent
expressions of one disorder. Other cutaneous findings of
DDD include perioral scars, comedo like papules, hidradenitis
suppurativa, keratoacanthoma, multiple cysts and abscesses.
RAPK can be associated with palmoplantar keratoderma,
acrokeratoelastodosis, alopecia areata, nevus spilus, nevus
anaemicus and bilateral talipes. CONCLUSION This case is
presented for rare the association of DDD and RAPK.
Keyword :Dowling Degos Disease, Reticulate
Acropigmentation of Kitamura
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