A case of Hemi-Convulsions- HHE Syndrome
Abstract
Hemiconvulsion-Hemiplegia-epilepsy
syndrome (HHE) is focal epilepsy, a rare
epileptic syndrome characterized by prolonged
partial epilepsy producing hemiplegia
sometimes followed by epilepsy
disorder(1). We report 19 yr male with
right hemiplegia, history of prolonged
unilateral seizures since 4yrs of age, with
evidence of left hemispheric atrophy on
magnetic resonance imaging (MRI).The
pathogenesis of HHE syndrome is likely
to be due to histotoxic epileptic brain
damage following prolonged focal convulsion
due to any cerebral insult (2).
Here we present a case of Idiopathic
HHE syndrome related to poorly treated
febrile seizures in childhood.
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