Anaesthetic Management of a Parturient with Charcot Marie Tooth Disease for Emergency LSCS
Abstract
Charcot Marie Tooth disease belongs to a group of hereditary sensorimotor neuropathies caused by a specific mutation in one of the several genes for myelin resulting in defects in the structure and function of myelin. The disease is characterised by progressive muscle atrophy, sensory and motor deficits in all four limbs. The anaesthetic experience for this group of diseases is limited to a few case reports and retrospective reviews. Most reports have indicated that major challenges with general anaesthetic administration in CMTD patients are the appropriate use of non-depolarizing muscle relaxants and preparation for malignant hyperthermia in neuromuscular disease.
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