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An Intersting Case of Myelopathy – A Case Report

Rekha R .

Abstract


Hirayama disease, also known as monomelic           amyotrophy (MMA), is a rare cervical myelopathy that              manifests itself as a self-limited, asymmetrical, slowly          progressive atrophic weakness of the forearms and hands predominantly in young males. The forward displacement of the posterior dura of the lower cervical dural canal during neck flexion has been postulated to lead to lower cervical cord atrophy with asymmetric flattening. We report a case of           Hirayama disease in a 30-year-old  man presenting with gradually progressive asymmetrical weakness and wasting of both hands and forearms.

 Keywords  : Hirayama’s disease, Posterior Dural sac, MRI cervical spine

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References


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