An Unusual Cause For ExtraHepatic Portal Vein Obstruction– A Case Report
Abstract
Extra Hepatic Portal Vein Obstruction is defined as“a vascular disorder of liver,characterized by obstruction of the extra-hepatic PV with or without involvement of intra-hepatic PV radicles orsplenic or superior mesenteric veins”. Etiological factors differ among pediatric and adult populations.Despite extensive history and laboratory work-up,many cases have been labelled idiopathic.However in our patient we were able to identify a unusual cause for EHPVO.
Keywords:ExtraHepatic Portal Vein Obstruction, Systemic lupus erythematosus
Introduction
Extrahepatic portal vein obstruction is a vascular disorder of the liver, which can results in obstruction and cavernous transformation of the portal vein with or without involvement of intrahepatic portal vein, splenic vein, or superior mesenteric vein.Portal vein obstruction due to chronic liver disease,neoplasm, or post surgery is considered a separate entity and is not the same as extrahepatic portal vein obstruction
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