The “Occam’s Razor”- a rare presentation of lupus
Abstract
A 40-year-old hypertensive female presented with history suggestive of recurrent attacks of intestinal angioedema. She had mild anaemia, raised ESR, Low serum complements-C3&C4, serum C1 inhibitor level was normal with reduced function and Antinuclear antibody was positive. Hence, a diagnosis of acquired angioedema was made. She also had acute nephritic syndrome, renal biopsy showed lupus nephritis. Linking both she had acquired angioedema secondary to SLE. Lupus presenting as angioedema is rare and the acquired type even rarer.
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