Case Series on Follicular Dendritic Cell Sarcoma – A Rare Entity
Abstract
Follicular dendritic cell sarcomas (FDCS) are rare neoplastic proliferation of spindle to ovoid cells which can resemble normal follicular dendritic cellsmorphologically. FDCS commonly arise from lymph nodes, but at least one-third can occur in extranodal sites. Differential diagnosis can be varied as morphologicalfeatures can be similar to other malignancies, but theimmunophenotypic profile is distinct and crucial for diagnosis. Herein, we report a series of 5 cases of FDCS and review theetiopathogenesis, clinical features, histopathology, immunohistochemistry, differential diagnosis and treatment options for FDCS.
Keywords: FDCS – Follicular dendritic cell sarcomas,
IHC – Immunohisto chemistryFull Text:
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