Unicuspid unicommissural aortic valve: an extremely rare congenital anomaly
Abstract
Unicuspid aortic valve is a rare congenital malformation that usually presents in the 3rd to 5th decade of life and usually with severe aortic stenosis or regurgitation. It often requires surgical correction. Diagnosis can be made with 2- or 3-dimensional transthoracic or transesophageal echocardiography, cardiac computed tomography, or cardiac magnetic resonance imaging.
We report the case of a 40 year old male who was asymptomatic and was referred to our cardiovascular center for preoperative evaluation.
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Cemri M, Cengel A, Timurkaynak T. Pentacuspid aortic valve diagnosed by transoesophageal echocardiography. Heart 2000; 84:E9
Anderson R. H. Understanding the structure of the unicuspid and unicommissural aortic valve. J Heart Valve Dis. 2003; 12(6):670–3.
Anderson RH. Understanding the structure of the unicuspid and unicommissural aortic valve. J Heart Valve Dis. 2003; 12:670–673.
Moller JH, Nakib A, Eliot RS, Edwards JE. Symptomatic congenital aortic stenosis in the first year of life. J Pediatr. 1966; 69:728–734.
Mookadam F, Thota VR, Garcia-Lopez AM, et al. Unicuspid aortic valve in adults:
A systematic review. J Heart Valve Dis 2010; 19:79-85
Edwards J. E. Pathologic aspects of cardiac valvular insufficiencies. AMA Arch Surg. 1958; 77(4):634–49.
Roberts W. C., Ko J. M. Frequency by decades of unicuspid, bicuspid, and tricuspid aortic valves in adults having isolated aortic valve replacement for aortic stenosis, with or without associated aortic regurgitation. Circulation. 2005; 111(7):920–5.
Novaro G. M., Mishra M., Griffin B. P. Incidence and echocardiographic features of congenital unicuspid aortic valve in an adult population. J Heart Valve Dis. 2003; 12(6):674–8.
Brantley H. P., Nekkanti R., Anderson C. A., Kypson A. P. Three-dimensional echocardiographic features of unicuspid aortic valve stenosis correlate with surgical findings. Echocardiography. 2012; 29(8):E204–7
Gibbs W. N., Hamman B. L., Roberts W. C., Schussler J. M. Diagnosis of congenital unicuspid aortic valve by 64-slice cardiac computed tomography. Proc (Bayl Univ Med Cent) 2008; 21(2):139.
Debl K., Djavidani B.,Buchner S., Poschenrieder F., Heinicke N.,Schmid C. et al.Unicuspid aortic valve disease: magnetic resonance imaging study [in German] Rofo. 2008; 180(11):983–7.
Kang S. D., Seol S. H., Park B. M., Kim D. K., Kim K. H., Kim D. I. et al. Incidental diagnosis of the unicuspid aortic valve with ascending aortic aneurysm in an asymptomatic adult. J Cardiovasc Ultrasound. 2011; 19(2):102–4.
Svensson L. G., Adams D. H., Bonow R. O., Kouchoukos N. T., Miller D. C., O'Gara P. T. et al. Aortic valve and ascending aorta guidelines for management and quality measures. Ann Thorac Surg. 2013; 95(6 Suppl):S1–66.
Kurtz C. E., Otto C. M. Aortic stenosis: clinical aspects of diagnosis and management, with 10 illustrative case reports from a 25-year experience. Medicine (Baltimore) 2010; 89(6):349–79.
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