Scimitar syndrome- a case report

Abstract

Scimitar syndrome is a rare congenital anomaly. It is essentially a combination of pulmonary hypoplasia and partial anomalous pulmonary venous return (PAPVR). It occurs exclusively on the right side. Surgical correction should be considered in the presence of significant left to right shunt and pulmonary hypertension. This involves creation of an inter-atrial baffle to redirect the pulmonary venous return into the left atrium. Alternatively, the anomalous vein can be reimplanted directly into the left atrium. We report a case, where a 36-year old man presented with dyspnea during physical exertion due to scimitar syndrome, a very rare congenital anomaly.